Hypernatremic Dehydration Associated With Pyloric Atresia

Congenital pyloric atresia (CPA) is an extremely rare condition. It may be isolated or accompanied by other abnormalities. In isolated cases, prognosis is good but congenital pyloric atresia can be fatal depending on another anomali. The etiology is still unknown. Since familial cases were reported in literature, it is suggested that this disease might be inherited. In here, we reported a delayed diagnosed congenital pyloric atresia case that presented with hypernatremic dehydration.